Spina Bifida – Neural Tube Defect (NTD)
Included In This Lesson
Study Tools For Spina Bifida – Neural Tube Defect (NTD)
Outline
Overview
- Failure of the spine to form and close during the embryonic stage.
- Varying degrees of severity
- Most common
- Anencephaly
- Cerebrum and cerebellum are absent
- Usually incompatible with life
- Myelomeningocele
- Anencephaly
Nursing Points
General
- Types
- Spina bifida occulta
- Small gap in the spine
- No opening or protrusion
- Hair or dark spot might cover
- May go undiscovered
- Meningocele
- Sac of fluid protrudes through the baby’s back
- Does not contain the spinal cord
- Myelomeningocele
- Most severe
- Spinal cord, meninges, and nerves protrude through an opening in the baby’s back
- Covered by a thin membrane
- Spina bifida occulta
- Causes
- Genetic component
- Folic acid deficiency during pregnancy (whole grains, fortified cereals, leafy vegetables, fruit)
- Women of childbearing age should consume 0.4 mg of folic acid daily
Assessment
- Assess spine at birth for anomalies
- Assess for motor and sensory disturbances
- Paralysis of lower extremities
- Motor impairment
- Assess for bowel and urinary incontinence
- Incontinence
- Lack of bowel control
- Assess for Joint deformities
- Club foot
- Hip dislocation
- Assess for other associated defects
- Hydrocephalus
- Bulging fontanels
- Measure head daily
- Hydrocephalus
Therapeutic Management
- Pre-Op Care
- Cover the sac with moist, sterile, non adherent dressings immediately.
- Change and keep clean
- Place infant in prone position with hips flexed to prevent damage to sac
- Assess size, shape, and color of sac and assess for changes
- Keep infant warm
- Increased risk for hypothermia
- Provide latex free environment
- Increase risk for developing allergy due if repeatedly exposed to it
- Cover the sac with moist, sterile, non adherent dressings immediately.
- Surgical repair/closure
- Within 24-72 hours
- Replace spinal cord and meninges and prevent further nerve damage
- Application of shunt to allow for CSF drainage
- Long-term Care
- Orthopedic care of MSK problems
- Management of neurogenic bladder and incontinence
- Clean intermittent Catheterization
- Oxybutynin chloride
- Vesicostomy
- Management of bowel incontinence
- Prevent constipation and impaction
- Fluids
- Fiber
- Laxatives
- Regular toileting habits
- Prevent constipation and impaction
- Transitioning to adulthood
- Independent living
- Having sexual relationships
- Child bearing
Nursing Concepts
- Functional Ability
- Mobility
- Elimination
Patient Education
- Prevention- importance of folic acid for women of childbearing age
- 0.4 mg daily
[lesson-linker lesson=”221529″ background=”white”]
ADPIE Related Lessons
Related Nursing Process (ADPIE) Lessons for Spina Bifida – Neural Tube Defect (NTD)
Transcript
Hey guys, in this lesson we are going to talk about Spina Bifida. Spina Bifida is a spinal cord or neural tube defect.
There is a spectrum of these neural tube defects that vary in terms of severity. The two most common are anencephaly and myelomeningocele. Anencephaly is the most severe neural tube defect and both the cerebellum and cerebrum are missing. This is usually incompatible with life.
The other three, are depicted in the photo. Spina bifida occulta isn’t usually visible from the outside. There’s a small gap in the spine, but no opening on the skin. There may be hair or dark skin over the site.
A meningocele is a larger gap in the spine where a sac of fluid protrudes through the skin. A myelomeningocele is when spinal cord, meninges and nerves are protruding in the sac of fluid.
The cause of spina bifida is multifactorial. There seems to be a genetic element, but a huge factor is lack of folic acid in the mother’s diet. It is recommended that women of childbearing age take a supplement of folic acid daily, 0.4 mg, to help prevent spina bifida from occurring.
Spina bifida is usually discovered either during a neonatal ultrasound or at birth during the neonatal assessment. Symptoms will vary with each patient, but if it is a myelomeningocele, and the spinal column and nerves are protruding the patient will have some amount of paralysis and sensory loss, as well as bowel and bladder dysfunction. So it’s important, that during our nursing assessment of this newborn, we are looking for movements and response to touch. We also need to keep a close eye on bowel and bladder function. They may have a meconium ileus and become constipated. They may also have bladder distention from the neurogenic bladder.
Joint deformities, like contractures and clubfoot are associated with spina bifida, as is hydrocephalus. So check all limbs and also perform a daily head circumference looking for hydrocephalus and increased intracranial pressure.
These babies will usually go to surgery within 24-72 hours of being born. Prior to surgery the top priority is to protect the protruding sac. It needs to be covered with a sterile, moist dressing. The baby needs to be kept in the prone position with hips flexed to reduce pressure and strain. They are at risk for hypothermia so they will usually be in an infant warmer. Never take a rectal temp in a newborn, but especially if they have spina bifida because they are at increased risk for having rectal anomalies.
They may need intermittent catheterization if their bladder becomes distended. And remember, kids with spina bifida are more likely to develop latex allergies so always double check that the equipment is latex free.
Once the malformation is repaired, our nursing care focuses on long-term management of the problems associated with the damage. This will vary per patient, but the most common issues are neurogenic bladder, neurogenic bowel and paralysis of lower extremities.
Both neurogenic bladder and bowel control require routine and careful planning to prevent problems. Clean intermittent catheterization is done periodically to empty the bladder and oxybutynin is given to decrease bladder spasms. Bowel control is achieved through scheduled evacuations that are planned according to the kids schedule. It’s important to prevent constipation with fiber, fluid intake and laxatives.
Often, these kids will have a wheelchair or other mobility devices to help maximize their independence. Your priority nursing concepts are functional ability, mobility and elimination.
Your key points for this lesson are- Knowing that spina bifida is a neural tube defect. There are a variety of diagnoses that fall under this category. The two most common are Anencephaly and myelomeningocele. Anencephaly is incompatible with life and myelomeningocele often causes the most symptoms because the spinal cord and nerves have protruded out of the spine into the sac.
The symptoms that occur with myelomeningocele are lower limb paralysis, bladder and bowel dysfunction and joint deformities.
These babies need surgery within a few days of being born. Prior to surgery the top priority for our nursing care is to protect the sac with a sterile, moist dressing and by positioning the patient on their stomach.
Long-term care is focused on bladder and bowel function and maximizing mobility and independence.
Patient education is super important. All women of childbearing age should take a folic acid supplement daily to help prevent these spinal malformations from occurring.
That’s it for our lesson on Spina Bifida. Make sure you check out all the resources attached to this lesson. Now, go out and be your best self today. Happy Nursing!